Bronchogenic cysts are an extremely rare congenital condition; their association with pericardial agenesis is even rarer. We describe the case of a 23-year-old patient who underwent an upper lobectomy to treat a bronchogenic cyst, with the incidental discovery of complete left pericardial agenesis. The association between bronchogenic cysts and pericardial agenesis is extremely rare, with only approximately 17 cases of this association have been reported in the literature to date. Pericardial agenesis on its own is one of the most rare cardiac malformations, with a prevalence of 0.044% described in a surgical series. Treatment of patients with pericardial agenesis is indicated for those with hemodynamic compromise or partial agenesis, although no difference has been observed in overall survival compared to the general population. In our patient, the defect was an incidental finding during surgery, and even though the heart was displaced secondary to the superior lobectomy, this did not cause hemodynamic deterioration. For this reason, we opted for conservative management. The patient is currently under follow-up with the cardiology department.

Adriana Simoneta Pimienta Ibarra, MD, is a general surgeon who completed her residency in 2020 at the Instituto Nacional de Ciencias Médicas y Nutrición “Salvador Zubirán.” She subsequently pursued specialized training in thoracic surgery, completing her fellowship at the Instituto Nacional de Enfermedades Respiratorias (INER) Ismael Cosío Villegas, where she served as chief resident. Currently she serves as an attending thoracic surgeon at INER, where she is an integral part of the Thoracic Surgery Department. Her academic contributions include authoring 11 peer-reviewed publications and 4 book chapters. Since 2022, Dr. Pimienta has been a member of the editorial board of the Journal of the Mexican Society of General Thoracic Surgeons. She also holds a leadership role as a member of the directive committee for thoracic surgery at the Latin American Thoracic Association (ALAT) and is a dedicated educator, serving as a professor of Anatomy for the Respiratory Therapy Degree program.